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Abstract Details

Diagnostic delay and challenges in a case of sarcoid myositis
Neuromuscular and Clinical Neurophysiology (EMG)
P15 - Poster Session 15 (5:30 PM-6:30 PM)
11-009

Sarcoidosis is a multisystem chronic granulomatous disease typically presenting with pulmonary manifestations. Extrapulmonary manifestations are less frequent. Sarcoid myositis is rare making it a diagnostic challenge. The case discussed will bring to attention the importance of keeping this entity among differential diagnoses for myositis. 

Describe diagnostic challenges in a case of sarcoid myositis

NA

Case description

48-year-old male evaluated for progressive polyarthralgia, myalgias and weakness. Patient was initially evaluated by Rheumatology. Laboratory studies revealed multiple positive antinuclear antibodies (ANA’s), positive ribonucleoproteins (RNP), SSA antibody, rheumatoid factor (RF), anti-neutrophil cytoplasmic antibodies (ANCA) and myeloperoxidase (MPO).  Differentials included discoid lupus, systemic lupus erythematosus versus mixed connective tissue given positive RNP treated with Plaquenil. He had a good response to few rounds of steroids. EMG was ordered revealing diffuse active myositis. Neurology was subsequently formally involved. Exam was significant for proximal more than distal muscles, muscle atrophy, contractures at the finger flexor joints, limitation with ambulation and inability to stand without assistance.  Respiratory symptoms prompted chest tomography which revealed hilar adenopathy. There was muscle edema on magnetic resonance. Muscle biopsy was notable for non-caseating granulomatous myositis confirming diagnosis of sarcoid myositis. Clinical improvement after chronic steroids were started. Alternative treatment considered was infliximab.

Discussion

Sarcoidosis is a multisystem chronic granulomatous disease most commonly affecting the lungs. Musculoskeletal manifestations occur in 20% of patients affecting mainly bone and rarely having isolated myopathy. Reports of random muscle biopsies in patients with systemic sarcoidosis have shown noncaseating granulomas in 32-80% of them. For extrapulmonary sarcoidosis, PET/CT and MRI are useful. Tissue biopsy will assist in providing a definitive diagnosis. Treatment is with steroids and/or steroid sparing immunosuppressants.

Sarcoid myositis is an underdiagnosed entity. Uncertainty in diagnosis can cause patient noncompliance with follow ups and treatment. This case elucidates the importance of diagnosis in a timely manner.

Authors/Disclosures
Maria Elisa Samaniego, MD
PRESENTER
Dr. Samaniego has nothing to disclose.
Paul T. Twydell, DO, FAAN (Corewell Health) Dr. Twydell has received publishing royalties from a publication relating to health care.
Anvita Potluri, MD Dr. Potluri has nothing to disclose.